Diagnosis:
Suggested by MRI and confirmed by pathology (brain biopsy/resection)
Clinical features:
occur in children < 2 years old
Findings on Investigations:
MRI:
- Supratentorial, superficial cortical
- Large cystic lesion with solid nodule, displacing normal brain
- Enhancing nodule
- May have dural attachment
Pathology:
May have dural attachment
Histology:
- Spindle cells in fascicles or storiform pattern. Large neurons in DIG. Also gemistocyte-like cells
- Dense reticulin network (reticulin or trichorme stains).
Immunohistochemistry: positive for GFAP, synaptophysin (in ganglion cells),